PHONE
+1-650-618-9889

International Journal of Clinical & Medical Images

ISSN: 2376-0249

Clinical-Medical Image - International Journal of Clinical & Medical Images (2018) Volume 5, Issue 8

Paget Disease of the Bone Presenting as Leontiasis Ossea

Paget Disease of the Bone Presenting as Leontiasis Ossea

Author(s): Carvalho Ruben*, Pereira Inês and Sapeira Isabel

10.4172/2376-0249.1000625

Clinical-Medical Image:

Paget disease of the bone is a chronic disorder of unknown etiology that typically results in enlarged, deformed bones due to abnormal and excessive bone remodeling. The disease which can be monostotic or polyostotic and is characterized initially by an increase in bone resorption, followed by a disorganized and excessive formation of bone, leading to pain, fractures, and deformities. The classically described radiological appearances are of expanded bone with a coarsened trabecular pattern, but it can present differently according to the disease stage: in the active or osteolytic phase, aggressive bone resorption and lytic appearance are the hallmarks while on the quiescent and inactive stage there is a predominance of cortical thickening and sclerosis, and finally, it can have a mixed pattern presentation. The pelvis, spine, skull, and proximal long bones are most frequently affected. We depict an exuberant case of this disease with craniofacial involvement resulting in the historical eponym of Leontiasis Ossea (lion mask face) (Figures 1 and 2).

flyer Image
Indexing and Archiving
A generic square placeholder image with rounded corners in a figure.
All published articles are assigned to Digital Object Identifier (DOI)- CrossRef.
A generic square placeholder image with rounded corners in a figure.
All published articles of this journal are included in the indexing and abstracting coverage of: